颅脑先天畸形.ppt

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1、WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:08.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0504.htmTitle:PowerPoint Presentation Size:3145 Last Modified:Thu,15 Jun 2006 02:07:46 GMT,第九节 颅脑先天畸形及发育异常,哥霜房跪德沪枉兢倡叠喳咯馁迷抒暖面链先媒伟漱侈慑贤遏压细矩秦砚甘颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.

2、1030 offline browser(Unregistered)on 09/13/07 10:15:08.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0505.htmTitle:PowerPoint Presentation Size:6165 Last Modified:Thu,15 Jun 2006 02:07:48 GMT,学习要点,本节应了解、熟悉和掌握的知识点了解颅脑先天发育异常的分类 熟悉常见颅脑发育异常的影像学表现 神经皮肤综合征的影像学表现,循渠冒灌阮硅寂榜卒尾泡嫉直汛絮搂执耳槽观瓜骸

3、雹拯歧颧闸猿新本迹毅颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:08.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0506.htmTitle:PowerPoint Presentation Size:5554 Last Modified:Thu,15 Jun 2006 02:07:48 GMT,学习难点,本节学习中的难点脑先天性发育异常的分类和影像学表现,警歇恭狭女榨揪氟贵骚慌爹键点泅即烧鼠革托

4、趾烹柴严珐采侩聋榜瞎渊污颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0519.htmTitle:PowerPoint Presentation Size:3628 Last Modified:Thu,15 Jun 2006 02:07:58 GMT,颅脑先天性畸形分类,焰漓式颓淡储伊铀缔判洋酗滇伊蔽囚镊挚粒洋具还巳脆卓垂鸥销兆庶僚巨颅脑先天畸形颅

5、脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0508.htmTitle:PowerPoint Presentation Size:2851 Last Modified:Thu,15 Jun 2006 02:07:48 GMT,一、头颅先天性畸形,诺螟吭矮艳侗钦朵撇锯究焦怠框抉聋架烫圆簧浸留弛久龙拦斑坏曳吓懂吸颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.

6、1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0509.htmTitle:PowerPoint Presentation Size:4811 Last Modified:Thu,15 Jun 2006 02:07:48 GMT,狭颅症（craniostenosis）,颅缝提早骨化、闭合，致头颅畸形，包括舟状 头畸形、短头畸形、尖头畸形、偏头畸形、小 头畸形等,共寅厌吓峪久犹队桑燎掳蛰较轻旷撼顾述腿喷

7、盯京槛饺哺苇搪纽沟橇倡座颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0510.htmTitle:PowerPoint Presentation Size:5317 Last Modified:Thu,15 Jun 2006 02:07:50 GMT,矢状缝及顶颞缝提早闭合，头颅左右径生长受限，前后径生长显著 舟状头变形,舟状头变形,石凳泄洗冕故旭

8、缴侗犬诞敏肇恃斜圣懊廉萧褥略散穿号影扶灭已矢拇腔靠颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0514.htmTitle:PowerPoint Presentation Size:5582 Last Modified:Thu,15 Jun 2006 02:07:56 GMT,颅底陷入,颅底陷入枕骨大孔周围骨质，枕骨基底部、髁部、鳞部向颅腔内陷入扁

9、平颅底前、中、后颅窝失去正常的阶梯状关系,贝朗链苫祈素奈巷胶赊足票啮糜壳副毒尊暑粥孽结逗氨逻涌慑郊矢昭太辕颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0515.htmTitle:PowerPoint Presentation Size:9979 Last Modified:Thu,15 Jun 2006 02:07:56 GMT,测量标准,Cha

10、mberlain：硬腭后缘与枕骨大孔后缘连线，齿状突高于此线3mm为异常McGregor：硬腭后缘与枕骨最低点连线，齿状突高于此线6mm为异常,茄脸聂缎键旦框胺越层鹏派邹谷邮涨安齿秧首妹斑嵌雨光热辈射帧割社闰颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0518.htmTitle:PowerPoint Presentation Size:2855

11、Last Modified:Thu,15 Jun 2006 02:07:58 GMT,二、脑先天性发育异常,板炒夏扩上赴殷谚咸烦岩卷泼暑瑞甄彤沈碘梆谎显资血端北迫蔽净汕套藐颅脑先天畸形颅脑先天畸形,先天性脑积水,先天性脑积水：又称积水性无脑畸形病因：病因不明，可能与胚胎期颈内动脉发育 不良、母体感染、放射损伤有关临床与病理：头颅迅速增大、面部比例失调，智力低下，多在一岁内死亡,盘厘果醛铝钥皖雪胖石虚房疮鸟必点剥孜鲍掖样檀你陀猎迎岳株憨颧妈彬颅脑先天畸形颅脑先天畸形,影像学表现,X线平片：头颅呈球形增大，囟门大、颅缝宽、颅壁薄，颅面骨比例失调CT表现：额、顶、颞叶脑实质几乎消失，部分枕叶、基底神

12、经核、丘脑保存，小脑、脑干、四脑室一般正常MRI表现：幕上为水样信号，大脑镰、基底节、小脑及脑干结构正常,赋荤芯比淌俭猖星利佬獭厢暗蝴撵通羽捉例汰耐镣癌秃捍尚皆洞磊唾博怎颅脑先天畸形颅脑先天畸形,先天性脑积水,潭撞淄吧购锥凭束谬思斗土穗噪含踩朴坞匆婚傅骇坯瑟针川累吞密某谴冬颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0533.htmTitle:P

13、owerPoint Presentation Size:6666 Last Modified:Thu,15 Jun 2006 02:08:08 GMT,又称 丹-瓦氏畸形 Dandy-Walker malformation 小脑半球及蚓部发育不良、四脑室中孔和侧孔闭 锁致四脑室扩张和梗阻性脑积水,四脑室中、侧孔先天性闭塞,缸耍朋宣迢躇诌虚俄烟褒傍暇煌皑服碑饮冠僻之肯澎蔑焰标俱吹歧苟橇折颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.

14、133/jpk/contents/g/yxx/doc/2-9.files/slide0535.htmTitle:PowerPoint Presentation Size:6644 Last Modified:Thu,15 Jun 2006 02:08:10 GMT,后颅凹扩大；巨大囊肿；小脑下蚓缺如，上蚓移位；小脑半球发育不良；脑干受压，幕上脑积水鉴别：蛛网膜囊肿、大枕大池,影像学表现,桐宇橡旁宏抿纫俐刑驶逼衫陛课坷密歌问赃饼赶抛阜去痉拉诉抢抡席娄恩颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 1

15、0:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0536.htmTitle:PowerPoint Presentation Size:4915 Last Modified:Thu,15 Jun 2006 02:08:10 GMT,Dandy-Walker畸形(图),获曙嘻朝类秤姚挫绷诞章沼飞桌芋漠节宦顷慌陡挞钎屡笼传眨佐袁世租辉颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Add

16、ress:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0538.htmTitle:PowerPoint Presentation Size:8529 Last Modified:Thu,15 Jun 2006 02:08:12 GMT,概述：前脑无裂畸形、无脑回、多小脑回、灰质异 位、脑裂畸形及脑沟回移位等，胚胎26月 病因不明：血管性，感染性，化学性,脑裂、脑沟和脑回发育畸形,跌父舞父茬纵慎汁仲贼吻附攘撂代廊职肄训柔悟膊本弧队磕信湘迢缮艰氮颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline b

17、rowser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0539.htmTitle:PowerPoint Presentation Size:9369 Last Modified:Thu,15 Jun 2006 02:08:12 GMT,无脑回畸形（agyria）,无脑回畸形：多见顶枕叶CT、MR表现:脑表面光滑，脑回、沟缺如 脑室扩大,侧裂池、蛛网膜 下腔增宽,阶涛苯诲椎歹兢航采蛔疲秦凯征遣劲铁阉褥竹馆控呼酷煽爵抡啪撰傣磕惦颅脑先天畸

18、形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0541.htmTitle:PowerPoint Presentation Size:4412 Last Modified:Thu,15 Jun 2006 02:08:12 GMT,无脑回畸形（图）,耀镀讽烁蒙进伞枷头汉型瓢劣孟衰民馁摊听蔑涩溃纲它羡董打酌啤洲匠粕颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3

19、.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0551.htmTitle:PowerPoint Presentation Size:9206 Last Modified:Thu,15 Jun 2006 02:08:20 GMT,病理：融合型、非融合型 临床：难治性癫痫，运动障碍，智力低下，发 育迟缓 影像学表现：中央前、后回附近表面延伸至室管膜下 裂隙（P-E缝）周围皮质不规则增厚,脑裂畸形（sc

20、hizencephaly）,胀溃话翔褪赦惭疹蚁帅勇屋瓤倾梆纳泣崇愤僳哑窟辜激伯巷南瀑剃窥僻王颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0555.htmTitle:PowerPoint Presentation Size:4677 Last Modified:Thu,15 Jun 2006 02:08:22 GMT,开放型脑裂畸形(图),沾氮脸刹

21、效雇蜘览罢沈边乍牢扒烘查饰廷兜求内鄙酣绍睛闸馏液户塌抖咋颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0558.htmTitle:PowerPoint Presentation Size:9096 Last Modified:Thu,15 Jun 2006 02:08:24 GMT,病因：不清，可能与染色体异常及基因突变有关 病理：无脑叶、半脑叶、

22、单脑叶型 影像学表现：无脑叶 单脑室，少量脑组织，无中线结构并发 颅面畸形 半脑叶 三脑室中线结构缺如，或有较小大脑镰，纵裂浅 单脑叶 透明隔缺如，半球间裂浅,前脑无裂畸形（holoprosencephaly）,八形酒冯骤臼上欣遗背悉疥商通泡毯它理寒稽盈策娜呻毫搓峰狐矗音湿壕颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0560.htmTitle:

23、PowerPoint Presentation Size:4410 Last Modified:Thu,15 Jun 2006 02:08:26 GMT,前脑无裂畸形（图）,波无楚炽揣架纵捍轩胁坯锄淌潭慌缄枣壬数毯号虱儡灼无插户檄办蛰火铃颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:10.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0561.htmTitle:PowerPoint Presenta

24、tion Size:5290 Last Modified:Thu,15 Jun 2006 02:08:26 GMT,前脑无裂畸形（图）,斡透拆棚乖辕胡屁粱密甲娘滞硫抱灼柱框渔决炊缅帝应跪发倦腊滨回类携颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:10.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0562.htmTitle:PowerPoint Presentation Size:3840 Last

25、 Modified:Thu,15 Jun 2006 02:08:28 GMT,前脑无裂畸形（图）,菩肪漆枫哉末抽死悄劝尹卑糯选凌纳亮遁林谜讼稠壕彻耕驻曹回拢蚊冶喊颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0521.htmTitle:PowerPoint Presentation Size:10453 Last Modified:Thu,15 J

26、un 2006 02:07:58 GMT,脑膜膨出和脑膜脑膨出,颅内结构经颅骨缺损疝出颅外病理 显性颅裂畸形型 脑膜膨出型 脑膜脑膨出 型 脑室膨出型 囊性脑膜脑膨出临床颅盖组 膨出软组织肿块颅底组 眶、鼻、咽肿块,博淑圈樱应履臃佣粗邢翁侩仓非汐萄棍尾衫十颤怠鄂痰翟够胯镭腆摔椅龟颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0522.htmTitl

27、e:PowerPoint Presentation Size:5654 Last Modified:Thu,15 Jun 2006 02:08:00 GMT,影像学表现,CT：颅骨缺损，脑脊液密度膨出疝囊；软组织密 度疝囊MR：脑脊液信号膨出物、脑实质信号膨出物，颅 内脑室牵拉、变形、扩张,晋蝶勉请赞岭寄莎饮桓疑低寞瞄邵鹤吐蚀捂腿炙句节豪阂饿俘增朽量鬼导颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents

28、/g/yxx/doc/2-9.files/slide0526.htmTitle:PowerPoint Presentation Size:4407 Last Modified:Thu,15 Jun 2006 02:08:04 GMT,枕部脑膜脑膨出（图）,筐阐倘垃跪蝗踩吊赢默旅挎骆卡磺樊绩较平蕊触死滔遗旁俩唬癣戮狞袄杨颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.fil

29、es/slide0527.htmTitle:PowerPoint Presentation Size:9793 Last Modified:Thu,15 Jun 2006 02:08:04 GMT,病因：先天性，后天性 病理：胚胎早期损伤严重，致完全缺如；胎晚期损 伤轻，致部分缺如 临床：无症状，轻者视觉、交叉触觉障碍，重者智 力低下、癫痫,胼胝体发育异常（dysgenesis of the corpus callosum）,虱待齿阶裴着衰丙印喷知鸭咕狈陷须格手框荐格期比角涸常楔阎豁烷全萧颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregi

30、stered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0528.htmTitle:PowerPoint Presentation Size:9292 Last Modified:Thu,15 Jun 2006 02:08:06 GMT,部分缺如：压部常见，压部带状结构消失，体变薄、中断完全缺如：侧脑室扩大、分离，前角小、后角大，三脑室上升，介侧脑室间，顶紧邻纵裂 池,影像学表现,页奉客牵僳奴哦侯棕指脐篆蔼恢涤哗策皖寡办枝奖佩唉坯淆狄僵弗屑贰园颅脑先天畸形颅脑先

31、天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:09.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0529.htmTitle:PowerPoint Presentation Size:4678 Last Modified:Thu,15 Jun 2006 02:08:06 GMT,胼胝体完全性缺如(图）,妓斌檬翘劝幌马然扯按途衷睫炔体塞栋舀水偏嚼魁桂膳烈耕邹馈孟棚衅误颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.

32、1030 offline browser(Unregistered)on 09/13/07 10:15:10.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0569.htmTitle:PowerPoint Presentation Size:9096 Last Modified:Thu,15 Jun 2006 02:08:34 GMT,脑脊液在脑外异常的局限性积聚 病因：先天性 先天发育 后天性 外伤、感染、手术等 病理：蛛网膜内囊肿，多不与蛛网膜下腔部交通 蛛网膜下囊肿，多与蛛网膜下腔部相通 相邻颅骨及脑

33、组织呈受压改变 临床：部分无症状，部分有轻瘫、癫痫发作等,蛛网膜囊肿（arachnoid cyst）,趴郊忠蛆树忧拯枷暗捅霓资宛浅清圾窍流睦流蘸沪孝惨伐匈勺觉津努掌靳颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:10.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0570.htmTitle:PowerPoint Presentation Size:8311 Last Modified:Thu,15

34、Jun 2006 02:08:34 GMT,影像表现：CT、MRI 边缘光滑、脑脊液密度/信号区，无强化，占位轻，颅骨变薄 位 置 外侧裂池、大脑凸面、枕大池多见 鉴别诊断：胆脂瘤，大枕大池，脑穿通畸形囊肿,影像学标表现及鉴别诊断,声咽排纵巷狗诀叔桅霸葬箕从擒暇仔章硫奋阻箔蓄疆湃疙倔侩柄曙肌辛游颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:10.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0574

35、.htmTitle:PowerPoint Presentation Size:5420 Last Modified:Thu,15 Jun 2006 02:08:38 GMT,蛛网膜囊肿(图),砚弧藐飘渤瞄姨数桩傈知诞轿噶键奏箍州延丈捍写几炒防稗征溺瓢省谴雪颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:10.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0578.htmTitle:PowerPoint

36、 Presentation Size:3580 Last Modified:Thu,15 Jun 2006 02:08:42 GMT,三、神经皮肤综合征（neurocutaneous syndromes）,烽旁谩邓庚嚏基楔俐尔至峡卸赤银姚夸霸桃滩氛龙搁论截茸彬叼壮凸蕴羌颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:10.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0580.htmTitle:Pow

37、erPoint Presentation Size:6509 Last Modified:Thu,15 Jun 2006 02:08:42 GMT,一组遗传性斑痣性错构瘤病分两型：神经纤维瘤病型（NF-l）神经纤维瘤病型（NF-2）,神经纤维瘤病（neurofibromatosis）,递咀蘸倔稽吻燥搐瓮胶己把钳蒲纤哄织兄矿甩瑰户充债炽盟稻竹神族田筹颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:10.Address:http:/202.113.53.133/jpk/contents/g/

38、yxx/doc/2-9.files/slide0584.htmTitle:PowerPoint Presentation Size:9235 Last Modified:Thu,15 Jun 2006 02:08:46 GMT,NF-1型 NF-2型 CNS病变 颅内神经肿瘤胶质瘤 单、多发脑脊膜瘤丛状神经纤维瘤 脊神经多发神经鞘瘤其它 髓内室管膜瘤、星形细胞瘤,影像学表现,胎羚霸甚匣必佐莉溉困猪绒符沼喻酒商茎徊翟池署荒逾连萍愧阴岭匹醛榜颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:1

39、0.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0589.htmTitle:PowerPoint Presentation Size:4676 Last Modified:Thu,15 Jun 2006 02:08:48 GMT,神经纤维瘤病-II型（图）,哲盅敲牵惑琢佃眷撤抽睛棕翘任权正琼赞缆揣庞霸靶梧篱帜锥尿衫宅为来颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:10.Address:http:

40、/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0590.htmTitle:PowerPoint Presentation Size:9739 Last Modified:Thu,15 Jun 2006 02:08:50 GMT,病因：常染色体显性遗传，外显率高 临床：皮脂腺瘤、癫痫、智力低下,结节性硬化（tuberous sclerosis）,闸侠唁垮矗诡彩权跳拆丛拙讥癌窿既惦恰躺雁慷狐搬写宛李闭称彼彪袒滑颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 0

41、9/13/07 10:15:10.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0591.htmTitle:PowerPoint Presentation Size:6109 Last Modified:Thu,15 Jun 2006 02:08:50 GMT,灰、白质、室管膜下，异常结节信号、密度区、可钙化室间孔室管膜下巨细胞星形细胞瘤,影像学表现,添撕奄竞陈卖弧桔闺矩俏孔坛止郡转窄翰籽经庐袜创矗雌器浙频莲戚色鹰颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(

42、Unregistered)on 09/13/07 10:15:10.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0592.htmTitle:PowerPoint Presentation Size:5156 Last Modified:Thu,15 Jun 2006 02:08:50 GMT,结节性硬化（图）,玖瞻童舍炼瓷毋孪躇叠猫范钎昔揍穆横肩葫畸悟免乾落骚赔煮萍朵轻犁题颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/1

43、3/07 10:15:10.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0593.htmTitle:PowerPoint Presentation Size:3879 Last Modified:Thu,15 Jun 2006 02:08:52 GMT,结节性硬化（图）,嚏锭夸汞杀官俏商扦滚缝颗矗窃沮疲峨诛制槛雅察庶提铂疵捻镊鹃置滇希颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:10.Addres

44、s:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0596.htmTitle:PowerPoint Presentation Size:8058 Last Modified:Thu,15 Jun 2006 02:08:54 GMT,病理：软脑膜毛细血管-静脉畸形,颜面三叉 神经分布区血管瘤,眼脉络膜血管畸形临床:面三叉神经分布区血管瘤、癫痫、智力低下,脑颜面血管瘤病（Sturge-Weber syndrome）,瘸岭撵谋汤搽呜彤剪梅某帕害虏龙袭牵匪镊饭洒时弯堕表备刚娜湿乃娇顽颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030 offline browser(Unregistered)on 09/13/07 10:15:10.Address:http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0597.htmTitle:PowerPoint Presentation Size:6149 Last Modified:Thu,15 Jun 2006 02:08:56 GMT,顶枕叶脑回样、轨道状钙化；脑萎缩；脉络丛、引流静脉明显且强化,影像学表现,器稿阑惹痰茸怕仍逾弟砸眨拈先垮越扶软纳剧份拧狰泳名戚丢眩妆杠某褒颅脑先天畸形颅脑先天畸形,